Primary immunodeficiency diseases: definition, diagnosis and management

Primary immunodeficiency disorders (PID) are a heterogeneous group of rare inherited conditions, caused by defects of different components of the immune system, and characterized by an unusual increased susceptibility to infections and a predisposition to autoimmunity and malignancy. As of different clinical and laboratory features of these disorders, PID involve different specialities and sub-specilities in addition to general practitionnaires. As of an increased trend in recognition and characterization of new types of PID, there is a need for all physician to be aware about such disorders. This book would be a practical book, describe the definition, etiology, clinical manifestations, diagnosis and management of all PID to increase awareness of all physicians regarding such disorders. This book would also provide excellent guidelines for diagnosis and treatment of patients, which are useful in clinical assistance to all patients and better health planning. Truly international Interdisciplinary Up-to-date INDICE: An introduction on primary immunodeficiency diseases.- Combined T-and B-cell immunodeficiencies.- Predominantly antibody deficiencies.- Other well-defined immunodeficiency syndromes.- Diseases of immune dysregulation.- Congenital defects of phagocyte number, function, or both.- Defects in innate immunity.- Autoinflammatory disorders.- Complement deficiencies.- New syndromic immunodeficiencies.- Treatment in primary immunodeficiency diseases.

• ISBN: 978-3-540-78537-8
• Editorial: Springer
• Encuadernacion: Cartoné
• Páginas: 210
• Fecha Publicación: 01/07/2008
• Nº Volúmenes: 1
• Idioma: Inglés