Von Willebrand disease: basic and clinical aspects

INDICE: List of Contributors. Foreword. Preface. 1 Historical perspective on von Willebrand disease (Erik Berntorp and Margareta Blombäck). 2 Biosynthesis and organization of von Willebrand factor (Sandra L. Haberichter). 3 von Willebrand factor Structure and Function (Robert R. Montgomery and Sandra L. Haberichter). 4 Modulation of von Willebrand factor by ADAMTS13 (Jennifer Barr andDavid Motto). 5 Animal models in von Willebrand disease (Cécile V. Denis, Olivier D. Christophe and Peter J Lenting). 6 Classification of von Willebrand Disease (Javier Batlle, Almudena Pérez-Rodríguez and María Fernanda López-Fernández). 7 The epidemiology of von Willebrand disease (Giancarlo Castaman and Francesco Rodeghiero). 8 Clinical Aspects of von Willebrand Disease: Bleeding History (Paula D. James and Alberto Tosetto). 9 Laboratory diagnosis of von Willebrand Disease: the phenotype (Ulrich Budde and Emmanuel J Favaloro). 10 Molecular Diagnosis of von Willebrand Disease: the Genotype (Anne C Goodeve and Reinhard Schneppenheim). 11 Clinical, Laboratory and Molecular Markers of Type 1 von Willebrand disease (David Lillicrap, Francesco Rodeghiero and Ian Peake). 12 Clinical, laboratory and molecular markers of von Willebrand disease type 2 (Dominique Meyer, Edith Fressinaud and Claudine Mazurier). 13 Clinical, laboratory and molecular markers of von Willebrand disease type 3 (Luciano Baronciani, Augusto B. Federici and Jeroen C.J. Eikenboom). 14 Pediatric Aspects of vonWillebrand Disease (Jorge Di Paola and Thomas Abshire). 15 Women with von Willebrand Disease (Christine A. Lee, Rezan A. Kadir and Peter A. Kouides). 16 The use of desmopressin in von Willebrand disease (Stefan Lethagen, Augusto B. Federici and Giancarlo Castaman). 17 The use of plasma-derived concentrates (Pier Mannuccio Mannucci, Massimo Franchini). 18 Prophylaxis in von Willebrand disease (Erik Berntorp). 19 Pathophysiology, Epidemiology, Diagnosis and Treatment of the Acquired von Willebrand Syndrome (Ulrich Budde, Augusto B. Federici and Jacob H. Rand). 20 Gene therapy for von Willebrand disease (Marinee K.L. Chuah, Inge Petrus and Thierry VandenDriessche).

• ISBN: 978-1-4051-9512-6
• Editorial: Wiley-Blackwell
• Encuadernacion: Cartoné
• Páginas: 280
• Fecha Publicación: 04/03/2011
• Nº Volúmenes: 1
• Idioma: Inglés